Hybrid peripheral nerve sheath tumor of parapharyngeal space having features of neurofibroma and schwannoma in an 8-year-old child – A rare entity :[PAUTHORS], Journal of Oral and Maxillofacial Pathology (JOMFP)

CASE REPORT
Year : 2022 | Volume : 26 | Issue : 5 | Page : 96--102

Hybrid peripheral nerve sheath tumor of parapharyngeal space having features of neurofibroma and schwannoma in an 8-year-old child – A rare entity

Himani Tiwari Chaturvedi¹, Chandrashekher Chaturvedi², Dipayan Jayanta Nandy²
¹ Department of Oral Pathology, Dharmsinh Desai University, Nadiad, Gujarat, India
² Department of Surgery, Gujarat Surgical Hospital, Vadodara, Gujarat, India

Correspondence Address:
Himani Tiwari Chaturvedi
A1/57, Darshanam greens, BH Baroda Public School 2, Near Nathdwara Residency, Dabhoi Waghodia Ring Road, Vadodara - 390 019, Gujarat
India

Tumors of the parapharyngeal space (PPS) are extremely rare in pediatric age group. Out of all head-and-neck neoplasms, PPS tumors comprise only 0.5%. Majority of neoplasms in poststyloid PPS are neurogenic tumors. Conventional benign peripheral nerve sheath tumor (PNST) includes neurofibromas, schwannomas and perineuriomas. Hybrid PNSTs are rare entities having combined features of more than one histologic type, and the World Health Organization Classification of Tumors of the Central Nervous System, in the latest 2016, 4^th edition, has recently recognized and published it. The most common hybrid tumor is schwannoma/perineuroma followed by neurofibroma/schwannoma and neurofibroma/perineuroma. Here, we are reporting a hybrid PNST which was completely excised and having combined features of neurofibroma and schwannoma, confirmed by both histopathologically and immunohistochemically, in an 8-year-old child, in PPS.

How to cite this article:
Chaturvedi HT, Chaturvedi C, Nandy DJ. Hybrid peripheral nerve sheath tumor of parapharyngeal space having features of neurofibroma and schwannoma in an 8-year-old child – A rare entity.J Oral Maxillofac Pathol 2022;26:96-102

How to cite this URL:
Chaturvedi HT, Chaturvedi C, Nandy DJ. Hybrid peripheral nerve sheath tumor of parapharyngeal space having features of neurofibroma and schwannoma in an 8-year-old child – A rare entity. J Oral Maxillofac Pathol [serial online] 2022 [cited 2023 Mar 29 ];26:96-102
Available from: https://www.jomfp.in/article.asp?issn=0973-029X;year=2022;volume=26;issue=5;spage=96;epage=102;aulast=Chaturvedi;type=0